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Table 2 Gives NIH consensus guidelines for type I neurofibromatosis diagnostic criteria

From: Neurofibroma involving obturator nerve mimicking an adnexal mass: a rare case report and PRISMA-driven systematic review

NIH consensus guidelines: diagnostic criteria for neurofibromatosis I. Two or more of the following  
1. Six or more cafe’-au-lait macules that are (in greatest diameter) > 5 mm in pre-pubertal individuals > 15 mm in post-pubertal individuals  
2. Two or more neurofibromas of any type, or one plexiform neurofibroma  
3. Axillary/inguinal freckling  
4. Optic glioma  
5. Two or more Lisch nodules  
6. Distinctive osseous lesion (i.e. sphenoid dysplasia or thinning of long bone cortex with or without pseudoarthrosis)  
7. First degree relative with NF-1