Table 1 Reports of MRKHS and Ovarian inguinal hernia published till date
Author | Age (yr) | Chief complaint/s | Diagnosis | Karyotype | Management | |
|---|---|---|---|---|---|---|
Elliot DC et al. (1989) [11] | 19 | Mass in left inguinal region × 2 years Pain and left groin bulge × 2 days, | Unicornuate uterus; inguinal hernia of fallopian tube, ovary and rudimentary uterine horn | 46, XX | Left pelvic kidney | Surgical exploration of left groin and resection of ovary, fallopian tube and rudimentary horn of uterus (Inguinal approach) |
Kriplani A et al. (2000) [12] | NA | Primary amenorrhea, | Mullerian agenesis with inguinal hernia of left horn of uterus and ovary | 46, XX | NA | |
Bazi et al. 2006 [13] | 12 | Cyclic alternating inguinal pain | Mullerian agenesis with bilateral inguinal ovaries | 46, XX | Left kidney seen at the level of right iliac fossa (crossed ectopia | Surgery suggested but deferred on patient’s wishes and started on low dose OCP to prevent cyclic inguinal pain |
Omari et al. (2011) [4] | 31 | Primary amenorrhea, infertility and dyspareunia | MRKH with utero-ovarian inguinal hernia | 46, XX | Single right pelvic kidney | Surgical exploration and reduction of hernia (Inguinal approach) + William vaginoplasty |
Demirel et al. (2012) [14] | 10 | Incidentally detected ovary in hernial sac during herniorrhaphy | MRKH type II with left ovarian hernia | 46, XX | Absent left kidney; cervical hemi-vertebra | Surgical exploration and reduction of hernia |
Palepu et al. (2015) [15] | 20 | Primary amenorrhea, bilateral groin swellings, acute onset of right-side pain | MRKH, bilateral tubo-ovarian hernia and right-side ovarian torsion | 46XX | laparotomy, herniorrhaphy, ovarian biopsy and repositioning of ovaries. | |
Mohanty et al. (2017) [16] | 20 | Primary amenorrhea | Mullerian agenesis (Type 1) with bilateral ovarian inguinal hernia | 46, XX | Bilateral ureteroceles | Not given details about surgery |
Verma R et al. (2018) [17] | 45 | Pain in inguinal area (started at age 43), primary amenorrhea | MRKHS | NA | Left kidney absent | Surgical exploration for resection of Mullerian duct remnants and hernia repair (Inguinal approach) |
Khan et al. (2019) [18] | 18 | Primary amenorrhea, swelling in left groin × 6 months, | MRKH | NA | Left renal agenesis | Laparoscopic total extraperitoneal repair of the ovarian inguinal hernia |
Jafari et al., (2020) [19] | 13 | Primary amenorrhea, swelling and pain in left groin | MRKHS, left inguinal hernia of ovary, fallopian tube and rudimentary horn of bicornuate uterus, | NA | Ectopia renal of left lower quadrant | Inguinal approach, repositioning of structures in pelvis and hernia repair |
Saini et al. [20] | 20 | Right inguinal swelling since 2 years of age, primary amenorrhea | MRKHS, unilateral lung agenesis, right inguinal ovarian hernia | 46, XX | Absent right kidney, fusion of posterior elements of 2nd- 7th cervical vertebral bodies; scoliosis | Inguinal approach, repositioning of structures in the pelvis and hernia repair |
Present Case | 17 | Primary amenorrhea, swelling in inguinal region since 2 years of age | MRKH, Turner’s Mosaic, inguinal hernia of left ovary and fallopian tube | 46XX (85%); 45XO (15%) | Ectopic and mal-rotated left kidney | Laparoscopic ovarian reposition and repair of hernial sac |